Jurnalul de Chirurgie
ISSN: 1584 - 9341
Vol.1 Nr.2 - aprilie - iunie 2005
 
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NUMARUL 2, VOL. 1, 2005

ARTICOLE ORIGINALE - ORIGINAL PAPERS

BENIGN SYMMETRIC LIPOMATOSIS - LAUNOIS-BENSAUDE SYNDROME OR MADELUNG'S DISEASE -
D. Gogalniceanu , Daniela Trandafir, Violeta Trandafir
Department of Oral and Maxillo-Facial Surgery
University of Medicine and Pharmacy „Gr.T. Popa” Iasi, Romania
Jurnalul de chirurgie 2005; 1 (2):190-195
Full text: Format PDF (Romanian)

Abstract:

Benign symmetric lipomatosis (BSL) is a rare proliferative disorder of the adipose tissue, characterized by symmetrical fat deposits, predominantly in the neck and shoulder area, upper back and arms.

A classification in three types according to the distribution of the pathological fatty was proposed by Donhauser (1991): type 1 (localized cervical fat proliferation); type 2 (pseudoathletic type); type 3 (gynecoid type).

METHODS: This study contains the analyse of a lot of ten patients with BSL, which were treated in our department between 1994 - 2004. The followed parameters were: sex, age, heredo-collateral antecedents, associated organic diseases, the motivation of medical addressability, the sites of first lesions, the length of evolution before the admission, methods for diagnosis, number of surgical sessions necessary to extirpation of fat deposits, the results of the periodic follow-up examination.

RESULTS: The followed patients with BSL were treated by surgery (extirpation of the inaesthetical cervical fat masses): one surgical session (8 cases); two sessions (2 cases). The follow-up examinations (clinical and laboratory tests) were accomplished at 3 months, 6 months, 1 year and 3 years (meanly regarding local recurrence). 8 cases: good results; 1 case: the associate peripheral neuropathy due to alcohol abuse made worse; 1 case: in course of pursuit. Recurrence at the site of surgery was not detected in any of the follow-up subjects. All of the patients were satisfied with the surgical result.

CONCLUSIONS: The elective treatment in BSL is surgical, by extirpation of the lipomatous masses; a satisfactory, lasting result can be expected only after the most radical possible extirpation (not only for cosmetic intentions ). Our study doesn't take down any local recurrence after the wide extirpations of the cervical disfigurement fat deposits (sometimes was necessary concomitent extirpation of the infiltrative structures - parotidectomy or submaxillectomy ).

KEYWORDS: MADELUNG' S DISEASE, MULTIPLE SYMMETRIC LIPOMATOSIS, BENIGN SYMMETRIC LIPOMATOSIS, SURGICAL TREATMENT IN BSL.

Correspondence: Prof. Dr. D. Gogalniceanu, Clinic Oral and Maxillo-Facial Surgery, „St. Spiridon” University Hospital Iasi, Independentei Street, no. 1, 700111, Iasi, Romania